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IHTIOZ

ihtiozIHTIOZ (Ichthyosis; yun. ichthys – mohi), mohipusti, bemorii irsii pust. Sababi on ikhtiloli ravandi shuga bastani pust ast. I. muqarrari va modarzod meshavad.
I.-i muqarrari nisbatan beshtar duchor meoyad. On dar sinni khurdsoli inkishof yofta, to davrai ba balogat rasidan avj megirad. Hangomi in shakli I. qarib tamomi pust (gayr az chinhoi kalon – orinj, zeri kash, qadkashak) zarar mebinad. Pusti illati khushk buda, bo qabathoi shugai khokistarrang faro girifta meshavad. Dar mavridi shakli sabuki bemori pust sabusak hosil mekunad; shakl nisbatan vaznini I. bo hosil shudani pulakchahoi gafs (diametrash to 1 sm) yo shugai sakhti jigari padid meoyad.
Ba I.-i modarzod ikhtiozi kudakon va eritrodermiyai ikhtiozmonand mansuband. I.-i kudak dar mohi seyumi inkishofi u dar batni modar ba vujud meoyad: pust bo qabati gafsi shuga faro girifta meshavad («kosai sangpusht»), uzvhoi dokhilii on purra inkishof nameyoband. CHunin kudakon mefavtand.
Eritrodermiyai ikhtiozmonand hangomi ba dunyo omadani tifl mushohida shuda, pust yakbora surkh megardad (bad tadrijan sabusak paydo mekunad). Bisyor vaqt pilki chashm rugardon (ektropion) va nokhunho gafs shuda, giperkeratozi kafi dastu po inkishof meyobad (gafs shudani shokhpardai epidermis); dar pust damidani obilachaho niz az ehtimol dur nest (I.-i epidermolizi). Dar bemoroni giriftori I. amrozi rimnoki pust niz paydo meshavand.
Muolijai I. duru daroz ast. Ba miqdori ziyod vitamini A, aevit tain karda meshavad; az usulhoi obshifoi va afkanishoti ultrabunafsh istifoda mekunand. Muntazam ba pust marhamhoi narmsozanda, inchunin marhami doroi mochevina va natriy khlor molidan lozim ast.
Farjomi bemori ba shakli I. vobastagi dorad. Hangomi I.-i muqarrari anjomi marizi khub ast; dar mavridi eritrodermiyai ikhtiozmonand bo guzashti sinnu sol zuhuroti bemori khele sabuk shavad ham, muolija nameyobad. Rohi peshgirii I. malum nest.
Ad.: Zoirov P. T., Bemorihoi pust, D., 1999; Hamon muallif, Bolezni koji, D., 2002; Hamon muallif, CHastnaya dermatologiya i venerologiya, D., 2007.
M. S. Isoeva..

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