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LIZOSOMAHO

lizosomahoLIZOSOMAHO, yake az unsurhoi hujayra. Qutrashon 0,2 – 2,0 mkm buda, bo parda faro girifta shudaand. Dar hujayra sadho L. vujud dorand. Vazifai asosii L. degidratatsiyai fermentii makromolekullaho va organellahoi ba hujayraho rohyofta meboshad. L.-i nakhustin dar dastgohi Golji hosil meshavand.
Paydoishi baze bemoriho ba nuqsi genetikii fermenthoi lizosomi vobasta ast, zero in fermentho dar degradatatsiyai glikogen (glikogenozho), lipidho (lipidozho) va proteoglikanho (mukopolisakharidozho) shirkat mevarzand.

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