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LEYKODISTROFIYA

leykodistrifiyaLEYKODISTROFIYA (az leyko… va trophe – tagziya), yak guruhi bemorihoi irsii silsilai asab, ki dar asnoi on moddai safedi magzi sar zarar mebinad. Ba L. leykodistrofiyai SHolts – Grinfild, leykodistrofiyai Peliseus – Mertsbekher, bemorii Aleksander va g. mansuband.
Alomathoi avvalini bemori dar sinni shirkhoragi, kudaki yo navrasi padid meoyand. Ikhtiloli harakat (ataksiya, falaji), nobinoi, demensiya, sar ba mushohida merasand. Dar mavridi baze shaklhoi L. mumkin ast silsilai asabi kanori niz illat paydo kunad. Farjomi bemori bad ast.

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