Home / Ilm / GALAKTOZA

GALAKTOZA

GALAKTOZA, monosakharid; yake az spirthoi shashatoma (geksozaho). G. dar ob nagz, dar spirt bad hal meshavad. Dar boftahoi nabotot G. dar tarkibi rafinozaho, molibiozaho, stakhiozho, hamchunin polisakharidho – galaktanho, moddahoi pektini, saponinho va g. duchor meoyad. Dar organizmi odam dar tarkibi laktoza (qandi shir), galaktogen, serebrozidho, mukoproteidho mavjud ast. Nig. niz Galaktozemiya.
GALAKTOZEMIYA (Galactosaemia; az galaktoza va lot. haima – khun), bemorii irsi. Dar natijai norasoii fermenthoe, ki baroi tajziyai galaktoza va ba glyukoza tabdil dodani on zarurand, paydo meshavad.
Ikhtiloli tajziyai galaktoza (nig. Karbogidratho) boisi dar khun gird omadani mahsuli mubodilai on megardad (mahsuli mubodila silsilai asabhoi markazi, jigar, gurdaho va chashmro zahrolud mesozad); dar chunin holatho gipoglikemiya niz rukh menamoyad. Dar ayni hol 3 navi G. mavjud ast: muqarrari, norasoii galaktokinazaho va epimerazaho.
Kudaki giriftori G.-i muqarrari kalon tavallud meshavad. Hangomi vaznin budani jarayoni marizi, badi ba dunyo omadan, tifl qay mekunad, az istemoli shir shikamrav meshavad; hamchunin zardparvin, kalon shudani jigar, katarakta ba mushohida merasand. Dar holathoi sabuk budani jarayoni marizi, kudak shirro hazm karda nametavonad, az sina ru megardonad.
Ba ivazi shir ba kudak omekhtahoi gizoi, khurokihoi shirii be laktoza, shavlahoi gushtiyu sabzavoti dodan lozim ast. Dar surati tabobat nakardan, kudakon badi chand moh mefavtand; hangomi rioya namudani parhez bemori nekfarjom ast.
Norasoii galaktokinazaho bo alomati katarakta padid meoyad; nishonahoi epimerazaho ba G.-i muqarrari monand meboshand. G.-hoi mazkur niz parhez mekhohand.

Инчунин кобед

afandi

LATIFAHO

TUYONA OYAD… SHakhse ba dustash uzr ovard:j – Bubakhsh, man ba tuyat rafta nametavonam. Vay …